Klinik fanlar yilnomasi Volume 2 Issue 4 (2025)
CLINICAL-NEUROLOGICAL STRATIFICATION OF PATIENTS WITH CONGENITAL AND SYSTEMIC SPINAL DISEASES: OPTIMIZATION OF MANAGEMENT TACTICS FOR SYRINGOMYELIA, FRIEDREICH'S ATAXIA, AND ARTERIOVENOUS MALFORMATIONS
Мирджураев Эльбек Миршавкатович, Адамбаев Зуфар Ибрагимович, Маматханова Чарос Баходировна
Abstract
Progressive motor disorders in 92%, POD in 76% (syringomyelia – 80%, AVM – 100%, Friedreich's ataxia – 58%). Stratification: Syringomyelia – surgery for cyst >4 mm/progression; conservative for stable forms. Friedreich's ataxia – predominantly conservative; surgery for scoliosis/stenosis. AVM – embolization/resection for bleeding risk; observation for asymptomatic cases. A treatment stratification based on pathology specificity and POD risk is proposed. A multidisciplinary approach optimizes outcomes.
syringomyelia, Friedreich's ataxia, spinal arteriovenous malformations, treatment stratification, neurosurgery, conservative therapy, pelvic organ dysfunction, Chiari malformation, scoliosis, multidisciplinary approach.сирингомиелия, атаксия Фридрейха, артериовенозные мальформации позвоночника, стратификация лечения, нейрохирургия, консервативная терапия, нарушение функции тазовых органов, аномалия Киари, сколиоз, мультидисциплинарный подход.siringomiyeliya, Fridreyx ataksiyasi, umurtqa arteriovenoz malformatsiyalari, davolash stratifikatsiyasi, neyroxirurgiya, konservativ terapiya, chanoq a'zolari funksiyasining buzilishi, Kiari anomaliyasi, skolioz, multiditsiplinar yondashuv.
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